Kasabach-Merritt syndrome, kaposiform haemangioendothelioma and platelet blockade

[Kaposiform haemangioendothelioma with Kasabach-Merritt phenomenon].

Kasabach-Merritt phenomenon is a serious coagulopathy associated with kaposiform hemangioendothelioma (KHE), tufted angioma, and possibly other vascular neoplasms. KHE presenting in the absence of Kasabach-Merritt phenomenon is rare, although tufted angioma frequently occurs without thrombocytopenia. We retrospectively reviewed 10 cases of KHE without Kasabach-Merritt phenomenon. The tumors app...

Kasabach-Merritt phenomenon in a neonatal kaposiform haemangioendothelioma.

To cite: Mardegan V, Doglioni N, De Bernardo G, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/bcr-2014205855 DESCRIPTION A female infant was born at 27 weeks of gestation through emergency caesarean section, performed because of an acute increase of a compressive thoracic malformation diagnosed at the 20th gestational week. At birth, two enormous violaceous m...

Kaposiform Hemangioendothelioma in a Newborn with Kasabach-Merritt Syndrome

Kasabach-Merritt syndrome.

Hemangiomas of infancy are usually congenital lesions. Occasionally they are associated with microangiopatbic bemolytic anaemia, thrombocytopenia, and a consumptive coagulopathy. This is most often associated with cavernous hemangiomas. Thrombocytopenia associated with giant cavernous hemangiomas was first noted by Kasabach and Merritt in 1940. As the primary mechanism of platelet destruction i...

kaposiform hemangioendothelioma in a newborn with kasabach-merritt syndrome

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